更多

供应


智慧城市网供应网 智慧交通 交通检测设备 测距仪芳香基硫酸酯酶1抗体

芳香基硫酸酯酶1抗体

  • 产地
  • 所在地
  • 美、英
  • 上海上海市

更新时间:2024-06-21

有效日期:还剩362

产品详情

更多抗体
我们提供的抗体用于实验研究,而不用于诊临床断或治疗程序。
芳香基硫酸酯酶1抗体Maintain refrigerated at 2-8°C for up to 6 months. For long term storage store at -20°C in small aliquots to prevent freeze-thaw cycles.
英文名称 Anti-ARSA
中文名称 芳香基硫酸酯酶1抗体
别 名 As 2; As2; ASA; metachromatic leucodystrophy; TISP73; arsA; ARSA_HUMAN; arylsulfatase A; Arylsulfatase A component C; AS A; Cerebroside-sulfatase; MGC125207; MLD.
浓 度 1mg/1ml
规 格 0.2ml/200μg
抗体来源 Rabbit
克隆类型 polyclonal
交叉反应 Human, Mouse, Rat
产品类型 一抗
研究领域 肿瘤 细胞生物 神经生物学 细胞类型标志物 细胞自噬
蛋白分子量 predicted molecular weight: 47/54kDa
性 状 Lyophilized or Liquid
免 疫 原 KLH conjugated synthetic peptide derived from human ARSA
亚 型 IgG
纯化方法 affinity purified by Protein A
储 存 液 Preservative: 15mM Sodium Azide, Constituents: 1% BSA, 0.01M PBS, pH 7.4
产品应用 WB=1:100-500 ELISA=1:500-1000 IP=1:20-100 IHC-P=1:100-500 IHC-F=1:100-500 IF=1:100-500
(石蜡切片需做抗原修复)
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
保存条件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
Important Note This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
产品介绍 The protein encoded by this gene hydrolyzes cerebroside sulfate to cerebroside and sulfate. Defects in this gene lead to metachromatic leucodystrophy (MLD), a progressive demyelination disease which results in a variety of neurological symptoms and ultimay death. Alternatively spliced transcript variants have been described for this gene. [provided by RefSeq, Dec 2010].
Function : Hydrolyzes cerebroside sulfate.
Subcellular Location : Lysosome.
Post-translational modifications : The conversion to 3-oxoalanine (also known as C-formylglycine, FGly), of a serine or cysteine residue in prokaryotes and of a cysteine residue in eukaryotes, is critical for catalytic activity. This post-translational modification is severely defective in multiple sulfatase deficiency (MSD).
DISEASE : Defects in ARSA are a cause of leukodystrophy metachromatic (MLD) [MIM:250100]. MLD is a disease due to a lysosomal storage defect. It is characterized by intralysosomal storage of cerebroside-3-sulfate in neural and non-neural tissues, with a diffuse loss of myelin in the central nervous system. Progressive demyelination causes a variety of neurological symptoms, including gait disturbances, ataxias, optical atrophy, dementia, seizures, and spastic tetraparesis. Three forms of the disease can be distinguished according to the age at onset: late-infantile, juvenile and adult.
Arylsulfatase A activity is defective in multiple sulfatase deficiency (MSD) [MIM:272200]. A clinically and biochemically heterogeneous disorder caused by the simultaneous impairment of all sulfatases, due to defective post-translational modification and activation. It combines features of individual sulfatase deficiencies such as metachromatic leukodystrophy, mucopolysaccharidosis, chondrodysplasia punctata, hydrocephalus, ichthyosis, neurologic deterioration and developmental delay. Note=Arylsulfatase A activity is impaired in multiple sulfatase deficiency due to mutations in SUMF1. SUMF1 mutations result in defective post-translational modification of ARSA at residue Cys-69 that is not converted to 3-oxoalanine.
Similarity : Belongs to the sulfatase family.
Database links : UniProtKB/Swiss-Prot: P15289.3
A18274 Soybean agglutinin,SBA ELISA Kit 大豆凝集素 96T
A18275 D2D (Rabbit D-Dimer) ELISA Kit 兔子D二聚体 96T
A18276 Phaseolus vulgaris agglutinin,PHA ELISA Kit 菜豆凝集素 96T
A18277 IL-1sR I (Rabbit soluble interleukin-1 receptor I ) ELISA Kit 兔子白介素1可溶性受体I 96T
A18278 Mouse eosinophil cationic protein,ECP ELISA Kit 小鼠嗜酸性粒细胞阳离子蛋白 96T
A18279 IL-32 ELISA Kit 大鼠白介素32 96T
A18280 Ep-CAM/CD362(Human Epithelial Cell Adhesion Molecule) ELISA Kit 人上皮细胞粘附分子 96T
A18281 PROGR ELISA kit 大鼠孕酮受体 96T
A18282 Lens culinaris agglutinin,LCA ELISA Kit 扁豆凝集素 96T
A18283 Mouse Qa lymphocyte antigen 2 region,Qa-2 ELISA Kit 小鼠Qa淋巴细胞抗原2 96T
A18284 Lep IgG (Rabbit Leptospira IgG) ELISA Kit 兔钩端螺旋体IgG 96T
A18285 Sam(Human soluble adhesion molecules) ELISA Kit 人可溶性粘附分子 96T
A18286 AmAC-1(Human Alternative macrophage activation-associated CC chemokine 1) ELISA Kit 人巨噬细胞替代激活相关化学因子1 96T
A18287 IL-21 ELISA Kit 大鼠白介素21 96T
A18288 Ricinus communis agglutinin,RCA ELISA Kit 蓖麻凝集素 96T
A18289 Mouse D-Lactate Dehydrogenase,D-LDH ELISA Kit 小鼠D-乳酸脱氢酶 96T
A18290 F1+2 (Rabbit prothrombin fragment 1+2) ELISA Kit 兔凝血酶原片段F1+2 96T
A18291 ADM (Rabbit soluble endothelial protein C receptor) ELISA Kit 兔子肾上腺髓质素 96T
A18292 D-LDH ELISA Kit 大鼠D-乳酸脱氢酶 96T
A18293 VEGFR-2/sFLK-1(Human soluble vascular endothelial growth factor receptor-2) ELISA Kit 人可溶性血管内皮生长因子受体2 96T
A18294 Pisum sativum agglutinin,PSA ELISA Kit 豌豆凝集素 96T
A18295 Rat Progesterone receptor,PROGR ELISA kit 小鼠孕酮受体 96T
A18296 Dolichos bifows agglutinin,DBA ELISA Kit 双花扁豆凝集素 96T
A18297 TSLP(Human thymic stromal lymphopoietin) ELISA Kit 人胸腺基质淋巴细胞生成素 96T
A18298 TARC/CCL17 ELISA Kit 大鼠胸腺活化调节趋化因子 96T
A18299 sEPCR (Rabbit soluble endothelial protein C receptor) ELISA Kit 兔子可溶性血管内皮细胞蛋白C受体 96T
A18300 Mouse Insulin-like growth factor binding protein 6,IGFBP-6 ELISA kit 小鼠胰岛素样生长因子结合蛋白6 96T
A18301 CH ELISA Kit 大鼠胆固醇 96T
A18302 Lp- Alpha (Rabbit lipoprotein Alpha) ELISA Kit 兔脂蛋白α 96T
A18303 PF/PFP(Human Perforin/Pore-forming protein) ELISA Kit 人穿孔素/成孔蛋白 96T
A18304 Plant calmodulin,CAM ELISA Kit 植物钙调素 96T
A18305 Mouse pulmonary activation regulated chemokine,PARC ELISA Kit 小鼠肺部活化调节趋化因子 96T
A18306 PTN(Human pleiotrophin) ELISA Kit 人多效生长因子 96T
A18307 Apo-E (Rabbit Apolipoprotein E) ELISA Kit 兔载脂蛋白E 96T
A18308 TG mouse ELISA Kit 小鼠甘油三酯 96T
A18309 Plant hormone abscisic acid,ABA ELISA Kit 植物激素脱落酸 96T
A18310 Mouse Lysozyme,LZM ELISA Kit 小鼠溶菌酶 96T
A18311 valosin-containing protein kit/VCP (human) 人含缬酪肽蛋白 96T
A18312 sCD28(human soluble cluster of differentiation 28) ELISA Kit 人可溶性CD28 96T
A18313 Mouse Beta-catenin, Beta-cat ELISA Kit 小鼠β连环蛋白/联蛋白 96T
A18314 LDL ELISA Kit 大鼠低密度脂蛋白 96T
A18315 Plant Vitamin K1,VK1 ELISA Kit 植物维生素K1 96T
A18316 apo-B100 (Rabbit apoprotein B100) ELISA Kit 兔载脂蛋白B100 96T
A18317 Plant Vitamin B12,VB12 ELISA Kit 植物维生素B12 96T
A18318 HDL ISA Kit 大鼠高密度脂蛋白 96T
A18319 Mouse pituitary adenylate cyclase activating polypeptide,PACAP ELISA Kit 小鼠垂体腺苷酸环化酶激活肽 96T
A18320 Human lymphocyte factor ELISA Kit 人淋巴细胞因子 96T
A18321 TGF Beta2 (Rabbit transforming growth factor Beta2) ELISA Kit 兔转化生长因子β2 96T
A18322 NOS (Rabbit nitric oxide synthase) ELISA Kit 兔一氧化氮合成酶 96T
A18323 Plant Vitamin A,VA ELISA Kit 植物维生素A 96T
A18324 Mouse Angiotensin converting enzyme,ACE ELISA Kit 小鼠血管紧张素转化酶 96T
A18325 TARC/CCL17(Human thymus activation regulated chemokine) ELISA Kit 人胸腺活化调节趋化因子 96T
A18326 PGR ELISA Kit 大鼠孕酮受体 96T
A18327 Mouse angiotension II ,ANG- II ELISA Kit 小鼠血管紧张素Ⅱ 96T
A18328 Plant Vitamin E,VE EELISA Kit 植物维生素E 96T
A18329 eNOS (Rabbit Endothelial nitric oxide synthase) ELISA Kit 兔内皮型一氧化氮合成酶 96T
A18330 NCAM-L1/CD171(Human Neural cell adhesion molecule ligand 1) ELISA Kit 人神经细胞粘附分子配体1 96T
A18331 ACE II ELISA Kit 大鼠血管紧张素Ⅱ转化酶 96T
A18332 ACE I ELISA Kit 大鼠血管紧张素Ⅰ转化酶 96T
数据奖励办法:如果您使用我公司发表了文献,并提交您发表文献的杂志信息,以及发表文献的有效网络链接与产品货号,您也将获得我公司以AM/AP开头的任意抗体小包装一支。
如果在您的实验中使用任何一款我公司一抗产品,并提交您的有效实验数据,您将获得我公司以AM/AP开头的任意抗体小包装一支。


免责声明:以上所展示的信息由企业自行提供,内容的真实性、准确性和合法性由发布企业负责,智慧城市网对此不承担任何保证责任。

发布询价单

上海晶抗生物工程有限公司

型:
生产厂家
联系人:
高经理

联系我时,请说明是在智慧城市网上看到的,谢谢

商家概况

主营产品:
ELISA试剂盒,鸭ELISA试剂盒,小鼠ELISA试剂盒,兔ELISA试剂盒,羊ELISA试剂盒,牛ELISA试剂盒,鸡ELISA试剂盒,猪ELISA试剂盒,猴ELISA试剂盒,犬ELISA试剂盒
公司性质:
生产厂家

该商家其它产品

moc1/moc2小鼠口腔鳞状细胞癌/雌性

moc1/moc2小鼠口...

摘要:口腔鳞状细胞癌(OSCC)是的 [详细]
HEP-53.4 小鼠肝癌细胞

HEP-53.4 小鼠肝...

摘要:来源于C57BL/6J小鼠的原发 [详细]
MOC2细胞系

MOC2细胞系...

摘要:MOC2细胞系由晶抗生物提供 [详细]
MOC1细胞系

MOC1细胞系...

摘要:MOC1细胞系在使用中,可增 [详细]
植物丙糖磷酸异构酶(TPI) elisa试剂盒

植物丙糖磷酸异构...

摘要:植物丙糖磷酸异构酶(TPI)el [详细]
植物丙二烯氧化物合酶(AOS) elisa试剂盒

植物丙二烯氧化物...

摘要:植物丙二烯氧化物合酶(AOS) [详细]
植物不饱和脂肪酸(USFA) elisa试剂盒

植物不饱和脂肪酸...

摘要:植物不饱和脂肪酸(USFA)eli [详细]
植物△1-吡咯啉-5-羧酸合成酶 elisa试剂盒

植物△1-吡咯啉-5...

摘要:植物△1-吡咯啉-5-羧酸合成 [详细]

其它商家同类产品